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1381530002: Fibro-adipose vascular anomaly (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 01-Dec 2025. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
5503811013 Fibro-adipose vascular anomaly en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5503812018 FAVA - fibroadipose vascular anomaly en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
5503813011 Fibro-fatty vascular anomaly en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5503814017 Fibroadipose vascular anomaly en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5503815016 Fibro-adipose vascular anomaly (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
5503816015 A rare vascular malformation characterised by fibro-adipose and venous tissue with diffuse muscle infiltration and extension along fascial planes, most often affecting the calf and forearm. Major clinical features include severe and persistent pain, phlebectasia, contractures, joint deformity as well as muscle atrophy. The skin is usually unremarkable. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5503817012 A rare vascular malformation characterized by fibro-adipose and venous tissue with diffuse muscle infiltration and extension along fascial planes, most often affecting the calf and forearm. Major clinical features include severe and persistent pain, phlebectasia, contractures, joint deformity as well as muscle atrophy. The skin is usually unremarkable. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Fibro-adipose vascular anomaly Is a Lesion of soft tissue (disorder) true Inferred relationship Some
Fibro-adipose vascular anomaly Is a Vascular disorder of extremity true Inferred relationship Some
Fibro-adipose vascular anomaly Is a Structural abnormality of adipose tissue (disorder) true Inferred relationship Some
Fibro-adipose vascular anomaly Finding site Fibrofatty tissue true Inferred relationship Some 1
Fibro-adipose vascular anomaly Associated morphology Fibrous overgrowth true Inferred relationship Some 1
Fibro-adipose vascular anomaly Associated morphology Morphologically abnormal structure (morphologic abnormality) true Inferred relationship Some 2
Fibro-adipose vascular anomaly Is a Abnormality of systemic vein (disorder) true Inferred relationship Some
Fibro-adipose vascular anomaly Finding site Venous structure of limb true Inferred relationship Some 2

Inbound Relationships Type Active Source Characteristic Refinability Group

Reference Sets

Component annotation with string value reference set (foundation metadata concept)

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